Cystic Fibrosis In Jordan : Clinical And Genetic Aspects
نویسنده
چکیده
Results: There were 37 males and 35 females in the study group. The mean age of all patients was 4.5 years; the mean age at presentation was 21.2 months; the mean age at diagnosis was 30.7 months and the mean delay of CF diagnosis was 9 months. Pancreatic exocrine insufficiency was documented in 94% of cases. Twenty (27%) children died, most below the age of 1 year. Pseudomonas aeruginosa was isolated in 30% of cases. Therapeutic measures were suboptimal in the majority of cases.
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تاریخ انتشار 2006